关键词: 生殖器肿瘤, 女（雌）性, 肉瘤, 妇科外科手术, 抗肿瘤联合化疗方案

Abstract: Sarcoma is a rare uterine malignant tumor with a high grade of malignancy and pool prognosis, which is easy to have local recurrence and distant metastasis. According to the different positions, pelvical sarcoma can have different subtypes, including uterine sarcoma, ovarian sarcoma, sarcoma of the cervix, vaginal, vulva and fallopian tubes. The mainstay of treatment is surgery, the principle is tumor reduction surgery. For uterine sarcoma, the mainstay of surgery is hysterectomy, for leiomyosarcoma（ＬＭＳ）, adnexectomy is not influencing the prognosis much, but for endometrial sarcoma（ＥＳＳ） and carcinosarcoma(CS), the mainstay is hysterectomy-bilateral oophorectomy, according to the different types and different stages, whether having lymphadenectomy or not is still in dispute, is lymphadenectomy helpful to the prognosis is controversial for years. Adjuvant therapy of pelvical sarcoma consists of chemotherapy, radiotherapy, hormonal therapy and target therapy which are at the exploratory stage. Because of the biological differences of different sarcoma subtypes, emphasizing the characteristic of sarcomas and individuation therapy is quite important.

Key words: Genital neoplasms, female, Sarcoma, Gynecologic surgical procedures, Antineoplastic combined chemotherapy protocols