Abstract: Granulosa cell tumours （GCTs） are relatively rare sex cord stromal tumours of the ovary. Most of them are hormone-producing，and can be initially diagnosed in early stage. Molecular biology markers are useful in diagnosis and follow-up. Surgery is an important treatment，while chemotherapy，radiotherapy，hormone therapy and molecular-targeted therapy also play important roles. With appropriate treatment，a better survival rate can be achieved against other ovarian malignancies.

Key words: Granulosa cell tumour, Ovarian neoplasms, Molecular biology, Leydig cell tumor, Therapy