关键词: Ebstein畸形, 心脏缺损, 先天性, 孕妇, 妊娠, 妊娠结局

Abstract:

Ebstein anomaly, also known as tricuspid valve subluxation malformation, is a rare congenital heart disease associated with tricuspid valve displacement and insufficiency. Pregnant women with Ebstein anomaly have a high risk of heart failure and arrhythmia due to changes in the cardiovascular system during pregnancy, which leads to adverse pregnancy outcomes and management challenges. We report two cases of Ebstein anomaly in pregnancy, one with cardiac Ebstein anomaly was detected during prenatal examination in early pregnancy, who presented with shortness of breath and other symptoms in mid to late pregnancy. She delivered a live baby by cesarean section at 37⁺¹ weeks of gestation after active monitoring and symptomatic treatment. The other case underwent surgery for atrial septal defect before pregnancy, there were no obvious cardiac symptoms during this pregnancy, and no cardiac ultrasound examination was performed. At 38⁺¹ weeks of pregnancy, she requested admission for cesarean section to terminate the pregnancy and Ebstein anomaly was detected during the examination. She delivered a live baby by cesarean section at 38⁺⁶ weeks of gestation. The two cases had good prognosis for both the mothers and the fetuses. Combining these 2 cases of pregnancy complicated with Ebstein anomaly and full-term delivery of live babies and reviewing the relevant domestic and international literature, to discuss and deepen the understanding of the disease, in order to better manage pregnant women with Ebstein anomaly.

Key words: Ebstein anomaly, Heart defects, congenital, Pregnant women, Pregnancy, Pregnancy outcome