Abstract: Extraovarian peritoneal serous papillary carcinoma is a kind of malignancy with its primary site in the peritoneum. The histological and cytological characteristics of the tumor resemble that of the ovarian papillary serous carcinoma. Its nidus is diffused in the perineum，but absent from the ovary or just superficially involved. The clinical manifestations of the patient are mainly non-specific symptoms of gastrointestinal tract，like the presentation of ovarian cancer in late stage. The definite diagnosis of extraovarian peritoneal serous papillary carcinoma is based on the pathologic manifestation and the events found in the surgery. The principle of treatment consists of cytoreductive surgery followed by cisplatin-based combined chemotherapy. In this review，we summarized the clinical manifestation，diagnosis and therapy of extraovarian peritoneal serous papillary carcinoma， to provide more evidence for future clinical application.

Key words: Carcinoma, papillary, Peritoneal neoplasms, Ovarian neoplasms, Antineoplastic combined chemotherapy protocols, Platinum compounds, Prognosis