Abstract: Objective：To discuss the ultrasound features and the correct diagnostic methods of congenital oblique vaginal septum syndrome（OVSS）. Method：To analyze clinical symptoms and ultrasound characteristics of 10 cases of OVSS confirmed by the operation. Results：All cases have double uterus，double cervix，haematocele and kidney absence on the oblique septum side.It’s difficult to make a diagnosis of OVSS during the pregnancy. Conclusions：The image characteristics of congenital OVSS are significant .Ultrasound can be used as a preferred and reliable method in diagnosis of OVSS.

Key words: Congenital abnormalities, Urogenital abnormalities, Ultrasonography, Oblique vaginal septum syndrome, Kidney absence